4A43

ICD-11 MMS 2026-01

Overlap or undifferentiated nonorgan specific systemic autoimmune disease

Description

Nonorgan specific systemic autoimmune diseases which do not fulfil the diagnostic criteria for any single recognised disease entity.

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A43.0 – IgG4 related disease
  • 4A43.1 – Mikulicz disease
  • 4A43.2 – Sjögren syndrome
  • 4A43.3 – Mixed connective tissue disease
  • 4A43.4 – Diffuse eosinophilic fasciitis
  • 4A43.Y – Other specified overlap non-organ specific systemic autoimmune disease
  • 4A43.Z – Undifferentiated non-organ specific systemic autoimmune disease

Sibling codes

  • 4A40 – Lupus erythematosus
  • 4A41 – Idiopathic inflammatory myopathy
  • 4A42 – Systemic sclerosis
  • 4A44 – Vasculitis
  • 4A45 – Antiphospholipid syndrome
  • 4A4Y – Other specified nonorgan specific systemic autoimmune disorders
  • 4A4Z – Nonorgan specific systemic autoimmune disorders, unspecified

Foundation entity

Overlap or undifferentiated nonorgan specific systemic autoimmune disease – http://id.who.int/icd/entity/636081762

Part of: 04: Diseases of the immune system