SAPHO syndrome

Description

SAPHO syndrome is characterised by a constellation of symptoms and signs including synovitis, acne conglobata or fulminans, palmoplantar pustulosis, hyperostosis and osteitis. Its aetiology is poorly understood.

Index terms

SAPHO syndrome
Pustulo-psoriatic hyperostotic spondylarthritis
SAPHO - [synovitis, acne, pustulosis, hyperostosis, osteitis] syndrome

Exclusions from above levels

02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Sibling codes

4A60 – Monogenic autoinflammatory syndromes
4A62 – Behçet disease
4A6Y – Other specified autoinflammatory disorders
4A6Z – Autoinflammatory disorders, unspecified

Foundation entity

SAPHO syndrome – http://id.who.int/icd/entity/1901494067

Part of: 04: Diseases of the immune system