Behçet disease

Description

Behçet disease is a disease of incompletely understood aetiopathogenesis characterised by recurrent oral and/or genital aphthous ulcers accompanied by cutaneous, ocular, articular, gastrointestinal, and/or central nervous system inflammatory lesions. Small vessel vasculitis, thrombotic vasculopathy, arteritis and arterial aneurysms may occur. It has a high prevalence from the Eastern Mediterranean across Central Asia to China and Japan.

Index terms

Behçet disease
Adamantiades-Behçet disease
Mucocutaneous Behçet disease

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Oropharyngeal ulceration due to Behçet disease
Anogenital ulceration due to Behçet disease
Ulceration of vulva due to Behçet disease
Ulceration of penis or scrotum due to Behçet disease
Penile or scrotal ulceration due to Behçet disease
Cutaneous manifestations of Behçet disease
Ocular Behçet disease
Behçet arthritis
Gastrointestinal complications of Behçet disease
Primary ulcer of small intestine in Behçet disease
Cardiovascular complications of Behçet disease
Neurological complications of Behçet disease

Inclusions

Adamantiades-Behçet disease

Exclusions from above levels

02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Sibling codes

4A60 – Monogenic autoinflammatory syndromes
4A61 – SAPHO syndrome
4A6Y – Other specified autoinflammatory disorders
4A6Z – Autoinflammatory disorders, unspecified

Foundation entity

Behçet disease – http://id.who.int/icd/entity/1668927157

Allowed postcoordination axes

Part of: 04: Diseases of the immune system