4B20

ICD-11 MMS 2026-01

Sarcoidosis

Description

Sarcoidosis is a multisystem disorder of unknown cause characterised by the formation of immune granulomas in involved organs. The lung and the lymphatic system are predominantly affected, but virtually every organ may be involved. Other severe manifestations result from cardiac, neurological, ocular, kidney or laryngeal localizations.

Exclusions from above levels

  • 2A83.0 – Monoclonal gammopathy of undetermined significance
  • NE84 – Failure or rejection of transplanted organs or tissues
  • 02 – Neoplasms
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4B20.0 – Sarcoidosis of lung
  • 4B20.1 – Sarcoidosis of lymph nodes
  • 4B20.2 – Sarcoidosis of the digestive system
  • 4B20.3 – Neurosarcoidosis
  • 4B20.4 – Ocular sarcoidosis
  • 4B20.5 – Cutaneous sarcoidosis
  • 4B20.Y – Other specified sarcoidosis
  • 4B20.Z – Sarcoidosis, unspecified

Sibling codes

  • 4B21 – Polyclonal hypergammaglobulinaemia
  • 4B22 – Cryoglobulinaemia
  • 4B23 – Immune reconstitution inflammatory syndrome
  • 4B24 – Graft-versus-host disease
  • 4B2Y – Other specified disorders involving the immune system

Foundation entity

Sarcoidosis – http://id.who.int/icd/entity/330792642

Allowed postcoordination axes

Part of: 04: Diseases of the immune system