5A13.1ICD-11 MMS 2026-01
Diabetes mellitus due to genetic defects in insulin action
Description
Other specified diabetes mellitus due to genetic defects in insulin action is a form of diabetes, which results from genetically determined abnormalities of insulin action. The metabolic abnormalities associated with mutations of the insulin receptor may range from hyperinsulinemia and modest hyperglycaemia to severe diabetes.
Index terms
- Diabetes mellitus due to genetic defects in insulin action
Exclusions from above levels
5A10– Idiopathic Type 1 diabetes mellitus5A11– Type 2 diabetes mellitusJA63– Diabetes mellitus in pregnancy
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18– Pregnancy, childbirth or the puerperium- http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn
Sibling codes
5A13.0– Diabetes mellitus due to genetic defects of beta cell function5A13.2– Diabetes mellitus due to diseases of the exocrine pancreas5A13.3– Diabetes mellitus due to endocrinopathies5A13.4– Diabetes mellitus due to drug or chemical5A13.5– Diabetes mellitus due to uncommon forms of immune-mediated diabetes5A13.6– Diabetes mellitus due to other genetic syndromes5A13.7– Diabetes mellitus due to clinically defined subtypes or syndromes5A13.Y– Diabetes mellitus due to other specified cause
Foundation entity
Diabetes mellitus due to genetic defects in insulin action – http://id.who.int/icd/entity/133436462
Allowed postcoordination axes
Part of: 5A13: Diabetes mellitus, other specified type › 05: Endocrine, nutritional or metabolic diseases