5A13.6

ICD-11 MMS 2026-01

Diabetes mellitus due to other genetic syndromes

Description

Other specified diabetes mellitus due to other genetic syndromes is a form of diabetes, which is associated with genetic syndromes.

Coding note

Use additional code, if desired, to identify any associated genetic syndrome

Index terms

  • Diabetes mellitus due to other genetic syndromes
  • MODY syndrome
  • MODY 1 syndrome
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  • maturity onset diabetes of the young type 1
  • MODY 2 syndrome
  • Maturity Onset Diabetes of the Young type 2
  • MODY 3 syndrome
  • Maturity Onset Diabetes of the Young type 3
  • MODY 4 syndrome
  • Maturity Onset Diabetes of the Young type 4
  • MODY 5 syndrome
  • ADTKD - [Autosomal Dominant Tubulointerstitial Kidney Disease] -HNF1B
  • Maturity Onset Diabetes of the Young type 5
  • Microdeletion 17q11.2
  • RCAD - [renal cyst and diabetes syndrome]
  • Renal cysts - Maturity-Onset Diabetes of the Young type 5 syndrome
  • Renal diabetes MODY 5 syndrome
  • Renal dysfunction - early-onset diabetes
  • MODY 6 syndrome
  • Maturity Onset Diabetes of the Young type 6
  • MODY 7 syndrome
  • Maturity Onset Diabetes of the Young type 7
  • MODY 8 syndrome
  • Maturity Onset Diabetes of the Young type 8
  • Wolcott-Rallison syndrome
  • Multiple epiphyseal dysplasia with early-onset diabetes mellitus

Exclusions from above levels

  • 5A10 – Idiopathic Type 1 diabetes mellitus
  • 5A11 – Type 2 diabetes mellitus
  • JA63 – Diabetes mellitus in pregnancy
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  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5A13.0 – Diabetes mellitus due to genetic defects of beta cell function
  • 5A13.1 – Diabetes mellitus due to genetic defects in insulin action
  • 5A13.2 – Diabetes mellitus due to diseases of the exocrine pancreas
  • 5A13.3 – Diabetes mellitus due to endocrinopathies
  • 5A13.4 – Diabetes mellitus due to drug or chemical
  • 5A13.5 – Diabetes mellitus due to uncommon forms of immune-mediated diabetes
  • 5A13.7 – Diabetes mellitus due to clinically defined subtypes or syndromes
  • 5A13.Y – Diabetes mellitus due to other specified cause

Foundation entity

Diabetes mellitus due to other genetic syndromes – http://id.who.int/icd/entity/1730828870

Allowed postcoordination axes

Part of: 5A13: Diabetes mellitus, other specified type › 05: Endocrine, nutritional or metabolic diseases