5A50.1

ICD-11 MMS 2026-01

Pseudohypoparathyroidism

Description

Pseudohypoparathyroidism is a condition with refractoriness to parathyroid hormone of its target tissues especially kidney that causes hypocalcaemia and hyperphosphataemia even in the presence of high circulating levels of biologically active parathyroid hormone.

Index terms

  • Pseudohypoparathyroidism
  • PHP - [pseudohypoparathyroidism]
  • constitutional chronic hypocalcaemia
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  • familial pseudohypoparathyroidism
  • parathyroid hormone resistant hypoparathyroidism
  • Pseudohypoparathyroidism with Albright hereditary osteodystrophy
  • AHO - [Albright hereditary osteodystrophy]
  • Albright hereditary osteodystrophy, classical type
  • Pseudohypoparathyroidism type 1A
  • Albright hereditary osteodystrophy - pseudohypoparathyroidism type 1A
  • pseudohypoparathyroidism type 1 A
  • pseudohypoparathyroidism type ia
  • Pseudohypoparathyroidism type 1C
  • Pseudohypoparathyroidism without Albright hereditary osteodystrophy
  • Pseudohypoparathyroidism type 1B
  • Pseudohypoparathyroidism type 2
  • Cataract in pseudohypoparathyroidism
  • Pseudopseudohypoparathyroidism
  • AHO - [Albright hereditary osteodystrophy] PPHP - [pseudopseudohypoparathyroidism]
  • Albright hereditary osteodystrophy - pseudopseudohypoparathyroidism

Exclusions from above levels

  • 5D42 – Postprocedural hypoparathyroidism
  • MB47.D – tetany NOS
  • 5B57 – Hypovitaminosis D
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  • 5C54.1 – Hyperphosphataemic familial tumoural calcinosis
  • 5C63.20 – Hypocalcaemic vitamin D dependent rickets
  • 5C63.21 – Hypocalcaemic vitamin D resistant rickets
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5A50.0 – Hypoparathyroidism due to impaired parathyroid hormone secretion
  • 5A50.Y – Other specified hypoparathyroidism
  • 5A50.Z – Hypoparathyroidism, unspecified

Foundation entity

Pseudohypoparathyroidism – http://id.who.int/icd/entity/1225154856

Allowed postcoordination axes

Part of: 5A50: Hypoparathyroidism › 05: Endocrine, nutritional or metabolic diseases