5A51.0

ICD-11 MMS 2026-01

Primary hyperparathyroidism

Description

Primary hyperparathyroidism is a condition with enhanced PTH (parathyroid hormone) secretion and high circulatory PTH level caused by abnormal parathyroid pathology such as adenoma, hyperplasia and cancer. Primary hyperparathyroidism usually causes hypercalcaemia by enhanced PTH actions.

Index terms

  • Primary hyperparathyroidism
  • parathyroid enlargement
  • Familial primary hyperparathyroidism
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  • Hereditary primary hyperparathyroidism
  • Familial isolated hyperparathyroidism
  • FIHPT - [familial isolated hyperparathyroidism]
  • Hereditary isolated hyperparathyroidism
  • Familial parathyroid adenoma
  • Hyperparathyroidism - jaw tumour syndrome
  • HPT-JT - [Hyperparathyroidism - jaw tumour syndrome]
  • Primary parathyroid hyperplasia
  • Familial parathyroid hyperplasia
  • Hereditary parathyroid hyperplasia
  • Neonatal severe primary hyperparathyroidism
  • Nonfamilial primary hyperparathyroidism
  • Non-hereditary primary hyperparathyroidism
  • Hyperplasia of parathyroid
  • parathyroid gland enlargement
  • parathyroid gland hyperplasia
  • parathyroid gland hypertrophy
  • parathyroid glandular hyperplasia
  • parathyroid glandular hypertrophy
  • parathyroid hypertrophy
  • Parathyroid osteitis
  • Brown tumour
  • fibro-osteoclasia
  • fibrous osteodystrophy
  • osteitis fibrosa cystica
  • osteitis fibrosa cystica generalisata
  • osteodystrophia fibrosa

Exclusions from above levels

  • 5B57.0 – infantile and juvenile osteomalacia
  • FB83.2 – Adult osteomalacia
  • 5B57 – Hypovitaminosis D
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  • 5C54.1 – Hyperphosphataemic familial tumoural calcinosis
  • 5C63.20 – Hypocalcaemic vitamin D dependent rickets
  • 5C63.21 – Hypocalcaemic vitamin D resistant rickets
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5A51.1 – Secondary hyperparathyroidism
  • 5A51.2 – Familial hypocalciuric hypercalcaemia
  • 5A51.Y – Other specified hyperparathyroidism
  • 5A51.Z – Hyperparathyroidism, unspecified

Foundation entity

Primary hyperparathyroidism – http://id.who.int/icd/entity/817194045

Part of: 5A51: Hyperparathyroidism › 05: Endocrine, nutritional or metabolic diseases