5A51.0ICD-11 MMS 2026-01
Primary hyperparathyroidism
Description
Primary hyperparathyroidism is a condition with enhanced PTH (parathyroid hormone) secretion and high circulatory PTH level caused by abnormal parathyroid pathology such as adenoma, hyperplasia and cancer. Primary hyperparathyroidism usually causes hypercalcaemia by enhanced PTH actions.
Index terms
- Primary hyperparathyroidism
- parathyroid enlargement
- Familial primary hyperparathyroidism
Show allHide
- Hereditary primary hyperparathyroidism
- Familial isolated hyperparathyroidism
- FIHPT - [familial isolated hyperparathyroidism]
- Hereditary isolated hyperparathyroidism
- Familial parathyroid adenoma
- Hyperparathyroidism - jaw tumour syndrome
- HPT-JT - [Hyperparathyroidism - jaw tumour syndrome]
- Primary parathyroid hyperplasia
- Familial parathyroid hyperplasia
- Hereditary parathyroid hyperplasia
- Neonatal severe primary hyperparathyroidism
- Nonfamilial primary hyperparathyroidism
- Non-hereditary primary hyperparathyroidism
- Hyperplasia of parathyroid
- parathyroid gland enlargement
- parathyroid gland hyperplasia
- parathyroid gland hypertrophy
- parathyroid glandular hyperplasia
- parathyroid glandular hypertrophy
- parathyroid hypertrophy
- Parathyroid osteitis
- Brown tumour
- fibro-osteoclasia
- fibrous osteodystrophy
- osteitis fibrosa cystica
- osteitis fibrosa cystica generalisata
- osteodystrophia fibrosa
Exclusions from above levels
Show allHide
5C54.1– Hyperphosphataemic familial tumoural calcinosis5C63.20– Hypocalcaemic vitamin D dependent rickets5C63.21– Hypocalcaemic vitamin D resistant rickets18– Pregnancy, childbirth or the puerperium- http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn
Sibling codes
Foundation entity
Primary hyperparathyroidism – http://id.who.int/icd/entity/817194045
Part of: 5A51: Hyperparathyroidism › 05: Endocrine, nutritional or metabolic diseases