ICD-11 MMS 2026-01
Other specified inborn errors of lipid metabolism
Exclusions from above levels
- http://id.who.int/icd/entity/1191191920 – Disorders of lipoprotein metabolism or certain specified lipidaemias
3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency5A71.01 – Congenital adrenal hyperplasia
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5A81.1 – 5-alpha-reductase deficiencyLD28.01 – Marfan syndromeLD28.1 – Ehlers-Danlos syndromeLD2A.4 – androgen resistance syndrome18 – Pregnancy, childbirth or the puerperium- http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn
Sibling codes
5C52.0 – Inborn errors of fatty acid oxidation or ketone body metabolism5C52.1 – Inborn errors of sterol metabolism5C52.2 – Neutral lipid storage disease5C52.Z – Inborn errors of lipid metabolism, unspecified
Part of: 5C52: Inborn errors of lipid metabolism › 05: Endocrine, nutritional or metabolic diseases