ICD-11 MMS 2026-01
Disorders of pyridoxine metabolism
Index terms
- Disorders of pyridoxine metabolism
Exclusions from above levels
- http://id.who.int/icd/entity/1191191920 – Disorders of lipoprotein metabolism or certain specified lipidaemias
3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency5A71.01 – Congenital adrenal hyperplasia
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5A81.1 – 5-alpha-reductase deficiencyLD28.01 – Marfan syndromeLD28.1 – Ehlers-Danlos syndromeLD2A.4 – androgen resistance syndrome18 – Pregnancy, childbirth or the puerperium- http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn
Foundation children elsewhere
8A61.00 – Pyridoxal dependent epilepsy
Sibling codes
5C59.0 – Disorders of biogenic amine metabolism5C59.1 – Disorders of gamma aminobutyric acid metabolism5C59.Y – Other specified inborn errors of neurotransmitter metabolism5C59.Z – Inborn errors of neurotransmitter metabolism, unspecified
Part of: 5C59: Inborn errors of neurotransmitter metabolism › 05: Endocrine, nutritional or metabolic diseases