5C90.2

ICD-11 MMS 2026-01

Liver diseases due to disorders of amino acid metabolism

Description

This is liver disease due to the disorder of the various biochemical processes responsible for the synthesis of proteins and amino acids, and the breakdown of proteins (and other large molecules, too) by catabolism.

Index terms

  • Liver diseases due to disorders of amino acid metabolism

Exclusions from above levels

  • DB92 – Non-alcoholic fatty liver disease
  • DB94 – Alcoholic liver disease
  • DB95 – Drug-induced or toxic liver disease
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  • JA65.0 – Acute fatty liver of pregnancy
  • 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
  • 5A71.01 – Congenital adrenal hyperplasia
  • 5A81.1 – 5-alpha-reductase deficiency
  • LD28.01 – Marfan syndrome
  • LD28.1 – Ehlers-Danlos syndrome
  • LD2A.4 – androgen resistance syndrome
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Foundation children elsewhere

  • 5C50.1 – Disorders of tyrosine metabolism
  • 5C50.A3 – Citrullinaemia

Sibling codes

  • 5C90.0 – Liver diseases due to urea cycle defects
  • 5C90.1 – Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport
  • 5C90.3 – Liver disease due to disorders of lysosomal storage
  • 5C90.4 – Liver diseases due to mitochondrial disorders
  • 5C90.5 – Liver diseases due to disorders of mineral metabolism
  • 5C90.Y – Other specified metabolic or transporter liver disease
  • 5C90.Z – Metabolic or transporter liver disease, unspecified

Foundation entity

Liver diseases due to disorders of amino acid metabolism – http://id.who.int/icd/entity/1276513691

Allowed postcoordination axes

Part of: 5C90: Metabolic or transporter liver disease › 05: Endocrine, nutritional or metabolic diseases