Dementia due to Alzheimer disease with early onset

Description

Dementia due to Alzheimer disease in which symptoms emerge before the age of 65 years. It is relatively rare, representing less than 5% of all cases, and may be genetically determined (autosomal dominant Alzheimer disease). Clinical presentation may be similar to cases with later onset, but progression of cognitive deficits may be more rapid.

Coding note

This category should never be used in primary tabulation. The codes are provided for use as supplementary or additional codes when it is desired to identify the presence of dementia in diseases classified elsewhere. When dementia is due to multiple aetiologies, code all that apply.

Coding note from above levels

This category should only be used for primary tabulation, if the aetiology of the dementia is unknown. If the aetiology of the dementia is known code to the aetiology of the dementia for primary tabulation. When dementia is due to multiple aetiologies, code all that apply.

Index terms

Dementia due to Alzheimer disease with early onset
Alzheimer disease dementia with early onset
Alzheimer type presenile dementia

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dementia in Alzheimer disease type 2
dementia in Alzheimer disease with early onset
early onset Alzheimer dementia
early onset Alzheimer type dementia, uncomplicated
presenile Alzheimer brain sclerosis
presenile brain sclerosis
presenile sclerosis
primary degenerative Alzheimer type dementia, early onset
primary degenerative Alzheimer type dementia, presenile onset, uncomplicated
Autosomal dominant Alzheimer disease dementia, mutation of presenilin 1
Autosomal dominant Alzheimer disease dementia, mutation of presenilin 2
Autosomal dominant Alzheimer disease dementia, mutation of amyloid precursor protein

Exclusions from above levels

6A00 – Disorders of intellectual development
6D70 – Delirium
http://id.who.int/icd/entity/1516623224 – Neurodevelopmental disorders

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MB20.0 – Stupor
MB20.1 – Coma
MG2A – Ageing associated decline in intrinsic capacity
QE62 – Uncomplicated bereavement
QE84 – Acute stress reaction

Sibling codes

6D80.1 – Dementia due to Alzheimer disease with late onset
6D80.2 – Alzheimer disease dementia, mixed type, with cerebrovascular disease
6D80.3 – Alzheimer disease dementia, mixed type, with other nonvascular aetiologies
6D80.Z – Dementia due to Alzheimer disease, onset unknown or unspecified

Foundation entity

Dementia due to Alzheimer disease with early onset – http://id.who.int/icd/entity/199015879

Allowed postcoordination axes

Part of: 6D80: Dementia due to Alzheimer disease › 06: Mental, behavioural or neurodevelopmental disorders