8A00.20

ICD-11 MMS 2026-01

Parkinsonism due to heredodegenerative disorders

Description

Parkinsonism may occur as a result of more widespread heredodegenerative disorders. It is accompanied by other neurological findings such as dystonia, ataxia and dementia. Other family members may be affected.

Index terms

  • Parkinsonism due to heredodegenerative disorders
  • Parkinsonism due to Neurodegeneration with brain iron accumulation NBIA
  • Parkinsonism due to spinocerebellar ataxias
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  • Parkinsonism in hereditary spastic paraplegia
  • Parkinsonism in Huntington disease
  • Parkinsonism in Wilson's disease
  • X-linked dystonia parkinsonism
  • Lubag

Exclusions from above levels

  • http://id.who.int/icd/entity/1425591047 – Myasthenia gravis or certain specified neuromuscular junction disorders
  • http://id.who.int/icd/entity/1525792972 – Arthropathies
  • 6A06 – Stereotyped movement disorder
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  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A00.21 – Hemiparkinsonism hemiatrophy syndrome
  • 8A00.22 – Infectious or postinfectious parkinsonism
  • 8A00.23 – Vascular parkinsonism
  • 8A00.24 – Drug-induced parkinsonism
  • 8A00.25 – Post traumatic Parkinsonism
  • 8A00.26 – Parkinsonism due to structural lesions
  • 8A00.2Y – Other specified secondary parkinsonism
  • 8A00.2Z – Secondary parkinsonism, unspecified

Foundation entity

Parkinsonism due to heredodegenerative disorders – http://id.who.int/icd/entity/1736055169

Allowed postcoordination axes

Part of: 8A00.2: Secondary parkinsonism › 8A00: Parkinsonism › 08: Diseases of the nervous system