8A01.11

ICD-11 MMS 2026-01

Chorea due to Huntington disease-like conditions

Description

The clinical picture of Huntington Disease (HD) is closely mimicked by disorders with an autosomal dominant inheritance. The gene test for HDS is negative prompting the consideration of other disorders. These are called HD like (HDL diseases).

Index terms

  • Chorea due to Huntington disease-like conditions
  • Chorea due to Huntington disease-like 1
  • Chorea due to Huntington disease-like 2
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  • Huntington disease-like 2
  • Chorea due to Huntington disease-like 3

Exclusions from above levels

  • 8A01.0 – Benign hereditary chorea
  • 6A06 – Stereotyped movement disorder
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A01.10 – Huntington disease
  • 8A01.12 – Chorea due to Dentatorubral pallidoluysian atrophy
  • 8A01.13 – Chorea due to Wilson disease
  • 8A01.14 – Chorea due to infectious or para-infectious causes
  • 8A01.15 – Chorea due to systemic lupus erythematosus
  • 8A01.16 – Drug-induced chorea
  • 8A01.1Y – Other specified secondary chorea
  • 8A01.1Z – Secondary chorea, unspecified

Foundation entity

Chorea due to Huntington disease-like conditions – http://id.who.int/icd/entity/58404408

Part of: 8A01.1: Secondary Chorea › 8A01: Choreiform disorders › 08: Diseases of the nervous system