8A02.0

ICD-11 MMS 2026-01

Primary dystonia

Description

Primary dystonias (primary torsion dystonias) are disorders where dystonia is the sole neurological manifestation. These disorders are slowly progressive and may be familial/genetic or sporadic in origin.

Exclusions from above levels

  • 8D21 – athetoid cerebral palsy
  • 6A06 – Stereotyped movement disorder
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8A02.00 – Benign essential blepharospasm
  • 8A02.0Y – Other specified primary dystonia
  • 8A02.0Z – Primary dystonia, unspecified

Sibling codes

  • 8A02.1 – Secondary dystonia
  • 8A02.2 – Paroxysmal dystonia
  • 8A02.3 – Functional dystonia or spasms
  • 8A02.Y – Other specified dystonic disorders
  • 8A02.Z – Dystonic disorders, unspecified

Foundation entity

Primary dystonia – http://id.who.int/icd/entity/557338504

Allowed postcoordination axes

Part of: 8A02: Dystonic disorders › 08: Diseases of the nervous system