8A02.12

ICD-11 MMS 2026-01

Dystonia associated with heredodegenerative disorders

Description

Dystonia occurring as a part of a more complex heredodegenerative disorder. It is not a pure dystonia and other neurological findings such as ataxia, pyramidal signs and cognitive issues may be seen.

Index terms

  • Dystonia associated with heredodegenerative disorders
  • Dystonia due to autosomal dominant disorders
  • Rapid-onset dystonia-parkinsonism
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  • Dystonia due to dentatorubropallidoluysian atrophy
  • Dystonia due to Huntington disease
  • Dystonia due to autosomal recessive disorders
  • Dystonia due to Wilson disease
  • Dystonia due to Niemann-Pick disease type C
  • Dystonia due to other autosomal recessive metabolic disorders
  • Dystonia due to GM2 gangliosidosis
  • Dystonia due to Metachromatic leukodystrophy
  • Dystonia due to homocystinuria
  • Dystonia due to glutaric acidaemia
  • Dystonia due to Hartnup disease
  • Dystonia due to ataxia-telangiectasia
  • Dystonia in neurodegeneration with brain iron accumulation type 1
  • Dystonia due to Juvenile Parkinson Disease including Parkin mutation
  • Probable autosomal recessive dystonia
  • Progressive pallidal degeneration
  • Dystonia due to X-linked dominant disorders
  • Dystonia due to Rett syndrome
  • Dystonia due to X-linked recessive disorders
  • Deafness-dystonia optic atrophy syndrome
  • Mohr-Tranebjærg syndrome
  • Dystonia due to Pelizaeus-Merzbacher disease
  • Dystonia due to Lesch-Nyhan syndrome
  • Dystonia due to mitochondrial cytopathies
  • Dystonia due to Leber's disease
  • Dystonia due to other mitochondrial cytopathies
  • Dystonia of variable inheritance
  • Dystonia due to Familial basal ganglia calcifications
  • Dystonia due to certain specified inherited disorders
  • Dystonia associated with familial basal ganglia calcifications
  • Dystonia due to isolated hereditary vitamin E deficiency
  • Dystonia due to hereditary spastic paraplegia
  • Dystonia 16
  • Infantile dystonia-parkinsonism

Exclusions from above levels

  • 8D21 – athetoid cerebral palsy
  • 6A06 – Stereotyped movement disorder
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A02.10 – Drug-induced dystonia
  • 8A02.11 – Dystonia-plus
  • 8A02.1Y – Other specified secondary dystonia
  • 8A02.1Z – Secondary dystonia, unspecified

Foundation entity

Dystonia associated with heredodegenerative disorders – http://id.who.int/icd/entity/803006786

Allowed postcoordination axes

Part of: 8A02.1: Secondary dystonia › 8A02: Dystonic disorders › 08: Diseases of the nervous system