8A21.0

ICD-11 MMS 2026-01

Posterior cortical atrophy

Description

Benson's syndrome or Posterior Cortical Atrophy (PCA) refers to a clinical syndrome in which higher order visual processing is disrupted owing to a neurodegenerative disorder. The patients present with progressive and severe visual agnosia (inability to recognize and identify familiar objects or persons) and apraxia (loss in the ability to execute or perform skilled familiar movements).

Index terms

  • Posterior cortical atrophy
  • Benson syndrome
  • Primary progressive apraxia
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  • Primary progressive visual-spatial impairment

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A21.Y – Other specified progressive focal atrophies
  • 8A21.Z – Progressive focal atrophies, unspecified

Foundation entity

Posterior cortical atrophy – http://id.who.int/icd/entity/377572273

Part of: 8A21: Progressive focal atrophies › 08: Diseases of the nervous system