8A22

ICD-11 MMS 2026-01

Lewy body disease

Description

Lewy body disease is a neurodegenerative disorder and the second most common form of dementia in the elderly after Alzheimer disease. Lewy bodies are histologically defined as intracytoplasmic eosinophilic neuronal inclusions in the cortex or brainstem.

Index terms

  • Lewy body disease
  • CLBD - [cortical Lewy body disease]
  • DLBD - [diffuse Lewy body disease]
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  • Lewy body
  • cortical Lewy body disease
  • diffuse Lewy body disease

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A20 – Alzheimer disease
  • 8A21 – Progressive focal atrophies
  • 8A23 – Frontotemporal lobar degeneration
  • 8A2Y – Other specified disorders with neurocognitive impairment as a major feature
  • 8A2Z – Disorders with neurocognitive impairment as a major feature, unspecified

Foundation entity

Lewy body disease – http://id.who.int/icd/entity/2091156678

Allowed postcoordination axes

Part of: 08: Diseases of the nervous system