8A61.41

ICD-11 MMS 2026-01

Progressive myoclonic epilepsy

Coding note from above levels

Use additional code, if desired, to identify the type of seizure.

Index terms

  • Progressive myoclonic epilepsy
  • Familial encephalopathy with neuroserpin inclusion bodies
  • Progressive myoclonic epilepsy type 1
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  • Unverricht-Lundborg disease
  • Progressive myoclonic epilepsy type 2
  • Lafora disease
  • Progressive myoclonic epilepsy type 3
  • Progressive myoclonic epilepsy type 6

Exclusions from above levels

  • MG45 – Syncope
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A61.40 – Reflex epilepsies
  • 8A61.4Y – Other specified genetic epileptic syndromes with variable age of onset
  • 8A61.4Z – Genetic epileptic syndromes with variable age of onset, unspecified

Foundation entity

Progressive myoclonic epilepsy – http://id.who.int/icd/entity/173613583

Part of: 8A61.4: Genetic epileptic syndromes with variable age of onset › 8A61: Genetic or presumed genetic syndromes primarily expressed as epilepsy › 08: Diseases of the nervous system