8B22.3

ICD-11 MMS 2026-01

Isolated cerebral amyloid angiopathy

Description

Cerebral amyloid angiopathy is characterised by the progressive accumulation of amyloid protein in the walls of small-to-medium-sized arteries and arterioles predominantly located in the leptomeningeal space, the cortex, and, to a lesser extent, also in the capillaries and veins.

Index terms

  • Isolated cerebral amyloid angiopathy
  • CAA - [cerebral amyloid angiopathy]
  • cerebrum amyloid angiopathy
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  • congophilic angiopathy
  • Familial dementia, British type
  • Familial dementia, Danish type
  • Hereditary amyloid precursor protein angiopathy
  • Hereditary cerebral haemorrhage with amyloidosis, Dutch type
  • Hereditary cerebral haemorrhage with amyloidosis, Icelandic type
  • Hereditary cystatin C amyloid angiopathy
  • Sporadic amyloid angiopathy

Exclusions from above levels

  • 8B25 – Late effects of cerebrovascular disease
  • NA07 – Intracranial injury
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8B22.0 – Dissection of cerebral arteries
  • 8B22.1 – Cerebral venous thrombosis
  • 8B22.2 – Cerebral vasoconstriction syndromes
  • 8B22.4 – Intracranial vascular malformation
  • 8B22.5 – Cerebral aneurysm, nonruptured
  • 8B22.6 – Familial cerebral saccular aneurysm
  • 8B22.7 – Cerebral arteritis, not elsewhere classified
  • 8B22.8 – Hypertensive encephalopathy
  • 8B22.9 – Migraine-induced stroke
  • 8B22.A – Subclavian steal syndrome
  • 8B22.B – Moyamoya syndrome
  • 8B22.C – Hereditary cerebrovascular diseases
  • 8B22.Y – Other specified cerebrovascular disease

Foundation entity

Isolated cerebral amyloid angiopathy – http://id.who.int/icd/entity/1502610635

Part of: 8B22: Certain specified cerebrovascular diseases › 08: Diseases of the nervous system