8B44.00

ICD-11 MMS 2026-01

Autosomal dominant hereditary spastic paraplegia

Index terms

  • Autosomal dominant hereditary spastic paraplegia
  • Autosomal dominant pure hereditary spastic paraplegia
  • Autosomal dominant pure hereditary spastic paraplegia due to mutations in Spastin gene
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  • Autosomal dominant spastic paraplegia type 10
  • Autosomal dominant spastic paraplegia type 12
  • Autosomal dominant spastic paraplegia type 13
  • Autosomal dominant spastic paraplegia type 19
  • Autosomal dominant spastic paraplegia type 3
  • Autosomal dominant spastic paraplegia type 31
  • Autosomal dominant spastic paraplegia type 4
  • Autosomal dominant spastic paraplegia type 42
  • Autosomal dominant spastic paraplegia type 6
  • Autosomal dominant spastic paraplegia type 8
  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant complex hereditary spastic paraplegia due to mutations in Spastin gene
  • Autosomal dominant spastic paraplegia type 29
  • Autosomal dominant spastic paraplegia type 37
  • Autosomal dominant spastic paraplegia type 38
  • Autosomal dominant spastic paraplegia type 9
  • Autosomal dominant spastic paraplegia type 17
  • Distal hereditary motor neuropathy type 5B
  • HMN5B
  • SPG17
  • Silver syndrome
  • Spastic paraplegia-amyotrophy of hands and feet

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8B44.01 – Autosomal recessive hereditary spastic paraplegia
  • 8B44.02 – X-linked hereditary spastic paraplegia
  • 8B44.0Y – Other specified hereditary spastic paraplegia
  • 8B44.0Z – Hereditary spastic paraplegia, unspecified

Foundation entity

Autosomal dominant hereditary spastic paraplegia – http://id.who.int/icd/entity/1547801209

Part of: 8B44.0: Hereditary spastic paraplegia › 8B44: Degenerative myelopathic disorders › 08: Diseases of the nervous system