ICD-11 MMS 2026-01
Neuromyotonia
Description
Neuromyotonia or Isaac's syndrome is an immune-mediated peripheral nerve disorder characterised by continuous muscle fibre activity at rest resulting in muscle stiffness, cramps, myokymia, and pseudomyotonia.
Index terms
- Neuromyotonia
- Isaacs neuromyotonia
- Isaacs syndrome
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- Isaacs-Mertens syndrome
- continuous muscle fibre activity
Exclusions from above levels
- http://id.who.int/icd/entity/155258022 – Metabolic disorders
LD26.41 – Arthrogryposis multiplex congenita05 – Endocrine, nutritional or metabolic diseases
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18 – Complications of pregnancy, childbirth and the puerperium19 – Certain conditions originating in the perinatal period22 – Injury, poisoning or certain other consequences of external causes
Sibling codes
8C71.0 – Myotonic dystrophy8C71.1 – Chondrodystrophic myotonia8C71.2 – Myotonia congenita8C71.3 – Drug-induced myotonia8C71.5 – Pseudomyotonia8C71.Y – Other specified myotonic disorders8C71.Z – Myotonic disorders, unspecified
Part of: 8C71: Myotonic disorders › 08: Diseases of the nervous system