8D87.0

ICD-11 MMS 2026-01

Multiple system atrophy

Description

Multiple system atrophy (MSA) is a rare neurodegenerative disorder characterised by varied combinations of parkinsonian, cerebellar, autonomic (erectile dysfunction, bladder dysfunction, orthostatic hypotension) and pyramidal features. The disease belongs to the group of alpha-synucleinopathies, a group of diseases characterised by aggregation of alpha-synuclein in affected brain regions. There are two different types: MSA-P (with parkinsonism) and MSA-C (with cerebellar dysfunction).

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8D87.00 – Multiple system atrophy, Cerebellar type
  • 8D87.01 – Multiple system atrophy, Parkinsonism
  • 8D87.0Y – Other specified multiple system atrophy
  • 8D87.0Z – Multiple system atrophy, unspecified

Sibling codes

  • 8D87.Y – Other specified autonomic nervous system disorder due to specified neurodegenerative disorder

Foundation entity

Multiple system atrophy – http://id.who.int/icd/entity/1890931931

Part of: 8D87: Autonomic nervous system disorder due to certain specified neurodegenerative disorder › 08: Diseases of the nervous system