8E4A.3

ICD-11 MMS 2026-01

Paraneoplastic or autoimmune disorders of the muscle

Description

Paraneoplastic and autoimmune diseases of muscle present with weakness and can be caused by a variety of causes, either by undefined remote effects or autoimmune effects in cancer, or autoimmune mechanisms in non cancer related conditions. The presentation is variable, usually presenting with a proximal myopathic pattern.

Index terms

  • Paraneoplastic or autoimmune disorders of the muscle
  • Paraneoplastic necrotising myopathy
  • Autoimmune necrotising myopathy
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  • Paraneoplastic hyperexcitability syndrome with continuous muscle fibre activity
  • Morvan syndrome
  • Autoimmune hyperexcitability syndrome with continuous muscle fibre activity or Morvan syndrome
  • Cancer sarcopenia or muscle wasting

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8E4A.0 – Paraneoplastic or autoimmune disorders of the central nervous system, brain or spinal cord
  • 8E4A.1 – Paraneoplastic or autoimmune disorders of the peripheral or autonomic nervous system
  • 8E4A.2 – Paraneoplastic or autoimmune neuromuscular transmission disorders
  • 8E4A.Y – Other specified paraneoplastic or autoimmune disorders of the nervous system
  • 8E4A.Z – Paraneoplastic or autoimmune disorders of the nervous system, unspecified

Foundation entity

Paraneoplastic or autoimmune disorders of the muscle – http://id.who.int/icd/entity/1129607960

Allowed postcoordination axes

Part of: 8E4A: Paraneoplastic or autoimmune disorders of the nervous system › 08: Diseases of the nervous system