AB33

ICD-11 MMS 2026-01

Otosclerosis

Description

Otosclerosis is a genetically mediated metabolic bone disease that affects the otic capsule and stapes. It is an autosomal dominant disorder with varying penetrance and expressivity. Usually symptomatic hearing loss from otosclerosis develops early in the third decade of life, although onset in the teenage years does occur.

Index terms

  • Otosclerosis
  • otospongiosis
  • Otosclerosis involving oval window, nonobliterative
Show allHide
  • nonobliterative otosclerosis
  • Otosclerosis involving oval window, obliterative
  • obliterative otosclerosis
  • Cochlear otosclerosis
  • Otosclerosis involving round window
  • Otosclerosis involving otic capsule

Inclusions

  • otospongiosis

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
Show allHide
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • AB30 – Acute vestibular syndrome
  • AB31 – Episodic vestibular syndrome
  • AB32 – Chronic vestibular syndrome
  • AB34 – Disorders of vestibular function
  • AB35 – Labyrinthine fistula
  • AB36 – Labyrinthine dysfunction
  • AB37 – Noise effects on inner ear
  • AB3Y – Other specified diseases of inner ear
  • AB3Z – Diseases of inner ear, unspecified

Foundation entity

Otosclerosis – http://id.who.int/icd/entity/1242649410

Allowed postcoordination axes

Part of: 10: Diseases of the ear or mastoid process