Chronic thromboembolic pulmonary hypertension

Description

Chronic thromboembolic pulmonary hypertension (CTEPH) is characterised by the persistence of thromboemboli in the form of organised tissue obstructing the pulmonary arteries. The consequence is an increase in pulmonary vascular resistance (PVR) resulting in pulmonary hypertension (PH) and progressive right heart failure.

Index terms

Chronic thromboembolic pulmonary hypertension
CTEPH - [chronic thromboembolic pulmonary hypertension]
Pulmonary hypertension with chronic thromboembolism

Exclusions from above levels

01 – Certain infectious or parasitic diseases
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth and the puerperium

Show allHide

19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations and chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

BB01.0 – Pulmonary arterial hypertension
BB01.1 – Pulmonary hypertension due to left heart disease
BB01.2 – Pulmonary hypertension due to lung disease or hypoxia
BB01.4 – Pulmonary hypertension with multifactorial mechanism
BB01.5 – Cor pulmonale
BB01.Z – Pulmonary hypertension, unspecified

Foundation entity

Chronic thromboembolic pulmonary hypertension – http://id.who.int/icd/entity/1567490107

Part of: BB01: Pulmonary hypertension › 11: Diseases of the circulatory system