BC42.3

ICD-11 MMS 2026-01

Rheumatic myocarditis

Description

Rheumatic myocarditis is cardiac inflammation and scarring triggered by an autoimmune reaction to group A streptococci infection resulting acutely in pancarditis involving inflammation of the myocardium, endocardium, and epicardium and chronically by valve fibrosis.

Index terms

  • Rheumatic myocarditis
  • dilated cardiomyopathy due to rheumatic fever
  • inactive or quiescent rheumatic fever with myocarditis
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  • inactive rheumatic myocarditis
  • myocardial degeneration with rheumatic fever
  • myocardial insufficiency with rheumatic fever
  • myocarditis due to rheumatic fever
  • rheumatic cardiomyopathy
  • rheumatic fibroid myocarditis
  • rheumatic interstitial myocarditis
  • rheumatic myocardial insufficiency
  • rheumatic progressive myocarditis

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • BC42.0 – Giant cell myocarditis
  • BC42.1 – Infectious myocarditis
  • BC42.2 – Hypersensitivity myocarditis
  • BC42.Y – Other specific myocarditis
  • BC42.Z – Myocarditis, unspecified

Foundation entity

Rheumatic myocarditis – http://id.who.int/icd/entity/1177212968

Allowed postcoordination axes

Part of: BC42: Myocarditis › 11: Diseases of the circulatory system