BC43.20

ICD-11 MMS 2026-01

Nonfamilial restrictive cardiomyopathy

Description

Nonfamilial restrictive cardiomyopathy is restrictive cardiomyopathy secondary to an acquired systemic disorder that is known to be associated with restrictive cardiomyopathy such as amyloidosis, scleroderma, sarcoidosis, or anthracycline therapy.

Index terms

  • Nonfamilial restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Restrictive cardiomyopathy due to endomyocardial abnormality
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  • Endomyocardial cardiomyopathy
  • Endomyocardial disease
  • Endomyocardial sclerosis
  • Endomyocardial fibrosis
  • African endomyocardial fibrosis
  • Davies disease
  • EMF - [endomyocardial fibrosis]
  • TEMF - [tropical endomyocardial fibrosis]
  • Tropical endomyocardial fibrosis
  • endomyofibrosis (deprecated)
  • Hypereosinophilic syndrome
  • constrictive endocarditis (deprecated)
  • Loeffler endocarditis
  • Endocarditis fibroplastica with eosinophilia
  • Endocarditis parietalis fibroplastica
  • Fibroplastic parietal endocarditis
  • Löffler parietal fibroplastic endocarditis
  • Myocarditis secondary to idiopathic hypereosinophilic syndrome
  • Primary eosinophilic Endomyocardial restrictive cardiomyopathy
  • Lymphocytic hypereosinophilic syndrome
  • Myeloproliferative hypereosinophilic syndrome
  • Restrictive cardiomyopathy due to radiation toxicity
  • Restrictive cardiomyopathy due to carcinoid syndrome
  • Restrictive cardiomyopathy due to scleroderma
  • Restrictive cardiomyopathy due to sarcoidosis
  • Restrictive cardiomyopathy due to drugs
  • Restrictive cardiomyopathy due to anthracycline toxicity
  • Wild type transthyretin-related amyloid cardiomyopathy
  • SSA - [senile systemic amyloidosis]
  • WTTA - [wild-type transthyretin amyloidosis]
  • senile systemic amyloidosis
  • wild type ATTR - [amyloid transthyretin] amyloidosis

Exclusions from above levels

  • BC42 – Myocarditis
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • BC43.2Y – Other specified restrictive cardiomyopathy
  • BC43.2Z – Restrictive cardiomyopathy, unspecified

Foundation entity

Nonfamilial restrictive cardiomyopathy – http://id.who.int/icd/entity/2097520643

Allowed postcoordination axes

Part of: BC43.2: Restrictive cardiomyopathy › BC43: Cardiomyopathy › 11: Diseases of the circulatory system