CA25.1

ICD-11 MMS 2026-01

Atypical cystic fibrosis

Index terms

  • Atypical cystic fibrosis
  • Pulmonary manifestations of atypical cystic fibrosis
  • Exacerbation of pulmonary manifestations of atypical cystic fibrosis
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  • Otorhinolaryngological manifestations of atypical cystic fibrosis
  • Digestive manifestations of atypical cystic fibrosis
  • Digestive haemorrhage in atypical cystic fibrosis
  • Distal ileal obstruction syndrome in atypical cystic fibrosis
  • Meconium ileus in atypical cystic fibrosis
  • Hepatic manifestations of atypical fibrosis
  • Elevated hepatic enzymes in atypical cystic fibrosis
  • Portal hypertension in atypical cystic fibrosis
  • Liver cirrhosis in atypical cystic fibrosis
  • Osteoporosis in atypical cystic fibrosis
  • Male infertility in atypical cystic fibrosis
  • Female hypofertility in atypical cystic fibrosis
  • Polyneuropathy in atypical cystic fibrosis

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • CA25.0 – Classical cystic fibrosis
  • CA25.2 – Subclinical cystic fibrosis
  • CA25.Z – Cystic fibrosis, unspecified

Foundation entity

Atypical cystic fibrosis – http://id.who.int/icd/entity/955958081

Allowed postcoordination axes

Part of: CA25: Cystic fibrosis › 12: Diseases of the respiratory system