CA71.3

ICD-11 MMS 2026-01

Lipoid pneumonitis

Description

Lipoid pneumonia (pneumonitis) refers to two types lipoid pneumonias (pneumonitises), one is Exogenous lipoid pneumonia (pneumonitis) and another is Endogenous lipoid pneumonia (pneumonitis). Exogenous lipoid pneumonia (pneumonitis) is the accumulation of aspirated oils within the alveoli and subsequent foreign body reaction. Endogenous lipoid pneumonia (pneumonitis), also called cholesterol pneumonia (pneumonitis) or golden pneumonia (pneumonitis), is a localised accumulation of lipid-laden macrophages within alveolar spaces distal to an obstructed airway.

Index terms

  • Lipoid pneumonitis
  • Lipoid pneumonia
  • Endogenous lipoid pneumonitis
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  • Endogenous lipoid pneumonia
  • Acute endogenous lipoid pneumonitis
  • Acute endogenous lipoid pneumonia
  • Chronic endogenous lipoid pneumonitis
  • Chronic endogenous lipoid pneumonia
  • Exogenous lipoid pneumonitis
  • Exogenous lipoid pneumonia
  • Acute exogenous lipoid pneumonitis
  • Acute exogenous lipoid pneumonia
  • Chronic exogenous lipoid pneumonitis
  • Chronic exogenous lipoid pneumonia
  • Hydrocarbon pneumonia

Exclusions from above levels

  • KB26 – Neonatal aspiration syndromes
  • CA40 – Pneumonia
  • CA23 – Asthma
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  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • CA71.0 – Pneumonitis due to inhalation of food or vomit
  • CA71.1 – Pneumonitis due to oils or essences
  • CA71.2 – Pneumonitis due to aspiration of blood
  • CA71.Y – Other specified pneumonitis due to solids or liquids
  • CA71.Z – Pneumonitis due to solids or liquids, unspecified

Foundation entity

Lipoid pneumonitis – http://id.who.int/icd/entity/1525086490

Allowed postcoordination axes

Part of: CA71: Pneumonitis due to solids or liquids › 12: Diseases of the respiratory system