DA90.1

ICD-11 MMS 2026-01

Congenital intestinal transport defect

Description

This is a congenital disease of the small intestinal mucosa that presents with intractable diarrhoea and malabsorption of nutrients in young children, due to defect of transporter of nutrients in enterocytes.

Index terms

  • Congenital intestinal transport defect
  • Congenital chloride diarrhoea
  • Congenital sodium diarrhoea

Exclusions from above levels

  • DE12.0 – Ileostomy malfunction
  • http://id.who.int/icd/entity/1195691020 – Diseases of duodenum
  • 01 – Certain infectious or parasitic diseases
Show allHide
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
  • 06 – Mental, behavioural or neurodevelopmental disorders
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Foundation children elsewhere

  • 5C61.0 – Glucose-galactose malabsorption
  • 5C61.40 – Fructose malabsorption
  • 5C64.20 – Acrodermatitis enteropathica

Sibling codes

  • DA90.0 – Syndromic diarrhoea
  • DA90.2 – Congenital intestinal motility disorders
  • DA90.Y – Other specified nonstructural developmental anomalies of small intestine
  • DA90.Z – Nonstructural developmental anomalies of small intestine, unspecified

Foundation entity

Congenital intestinal transport defect – http://id.who.int/icd/entity/671778206

Allowed postcoordination axes

Part of: DA90: Nonstructural developmental anomalies of small intestine › 13: Diseases of the digestive system