DB99.10

ICD-11 MMS 2026-01

Polycystic liver disease

Description

Polycystic liver disease is a genetic disorder characterised by the appearance of numerous cysts spread throughout the liver.

Index terms

  • Polycystic liver disease
  • PLD - [polycystic liver disease]
  • congenital polycystic disease of liver
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  • congenital polycystic liver disease
  • cystic disease of liver
  • cystic liver
  • multiple cysts of liver
  • polycystic liver
  • polycystic liver disorder
  • Autosomal dominant polycystic liver disease

Excludes

  • LB20.00 – Fibropolycystic liver disease

Exclusions from above levels

  • 5D00.0 – amyloid degeneration of liver
  • BD71.Y – hepatic vein thrombosis
  • DB94 – alcoholic liver disease
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  • DB95 – toxic liver disease
  • DB98.3 – portal vein thrombosis
  • LB20.00 – cystic disease of liver (congenital)
  • ME10.00 – hepatomegaly NOS
  • ME10.1 – Unspecified jaundice
  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
  • 06 – Mental, behavioural or neurodevelopmental disorders
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • DB99.1Y – Other specified hepatic cyst
  • DB99.1Z – Hepatic cyst, unspecified

Foundation entity

Polycystic liver disease – http://id.who.int/icd/entity/1361740083

Allowed postcoordination axes

Part of: DB99.1: Hepatic cyst › DB99: Certain specified diseases of liver › 13: Diseases of the digestive system