DC31.4

ICD-11 MMS 2026-01

Hereditary acute pancreatitis

Description

This is a recurrent acute inflammation of pancreas characterised by episodes of severe abdominal pain. Several genetic mutations are associated with this pancreatitis. Onset of the disease is generally under 20 years old, but it can be at any age.

Index terms

  • Hereditary acute pancreatitis
  • Hereditary acute pancreatitis, with local complication
  • Hereditary acute pancreatitis, with systemic complication
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  • Hereditary acute pancreatitis, with local and systemic complication

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 06 – Mental, behavioural or neurodevelopmental disorders
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • DC31.0 – Acute idiopathic pancreatitis
  • DC31.1 – Acute alcohol-induced pancreatitis
  • DC31.2 – Acute biliary pancreatitis
  • DC31.3 – Acute drug-induced pancreatitis
  • DC31.5 – Acute exacerbation of chronic pancreatitis
  • DC31.Y – Other specified acute pancreatitis
  • DC31.Z – Acute pancreatitis, unspecified

Foundation entity

Hereditary acute pancreatitis – http://id.who.int/icd/entity/927250371

Allowed postcoordination axes

Part of: DC31: Acute pancreatitis › 13: Diseases of the digestive system