DC32.2

ICD-11 MMS 2026-01

Hereditary chronic pancreatitis

Description

Hereditary chronic pancreatitis is a very rare form of childhood onset chronic pancreatitis. With the exception of an earlier onset and a slower progression the clinical course, the morphological features and laboratory findings of HCP do not differ from those present in patients with alcoholic chronic pancreatitis.

Index terms

  • Hereditary chronic pancreatitis

Exclusions from above levels

  • DC30.Y – Cystic fibrosis of pancreas with pancreatic insufficiency
  • DC35.2 – Pancreatic steatorrhoea
  • 01 – Certain infectious or parasitic diseases
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  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
  • 06 – Mental, behavioural or neurodevelopmental disorders
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • DC32.0 – Calcific pancreatitis
  • DC32.1 – Groove pancreatitis
  • DC32.3 – Chronic alcohol-induced pancreatitis
  • DC32.4 – Chronic idiopathic pancreatitis
  • DC32.5 – Tropical pancreatitis
  • DC32.Y – Other specified chronic pancreatitis
  • DC32.Z – Chronic pancreatitis, unspecified

Foundation entity

Hereditary chronic pancreatitis – http://id.who.int/icd/entity/1287702961

Allowed postcoordination axes

Part of: DC32: Chronic pancreatitis › 13: Diseases of the digestive system