EB03

ICD-11 MMS 2026-01

Syndromes with urticarial reactions or angioedema

Description

Periodic and other syndromes in which urticarial reactions or angioedema play an important part.

Index terms

  • Syndromes with urticarial reactions or angioedema
  • Schnitzler syndrome
  • Chronic urticaria with macroglobulinaemia
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  • Episodic angioedema with eosinophilia
  • Gleich syndrome

Exclusions from above levels

  • 2A21.10 – Urticaria pigmentosa
  • EK50.00 – Papular urticaria
  • 1B72.0 – Bullous impetigo of the napkin area
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  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
  • EH76 – Dermatoses associated with specific classes of medication

Foundation children elsewhere

  • 4A60.1 – Cryopyrin-associated periodic syndromes
  • 4A60.2 – Tumour necrosis factor receptor 1 associated periodic syndrome

Sibling codes

  • EB00 – Spontaneous urticaria
  • EB01 – Inducible urticaria or angioedema
  • EB02 – Cholinergic urticaria or related conditions
  • EB04 – Idiopathic angioedema
  • EB05 – Urticaria of unspecified type
  • EB0Y – Other specified urticarial disorders

Foundation entity

Syndromes with urticarial reactions or angioedema – http://id.who.int/icd/entity/927226833

Part of: 14: Diseases of the skin