EB13.0

ICD-11 MMS 2026-01

Stevens-Johnson syndrome

Description

Stevens-Johnson syndrome is an immune-complex–mediated hypersensitivity disorder involving mucous membranes (conjunctivae, oral mucosa and genital mucosa) with, by definition, skin involvement limited to no more than 9% body surface area. It is related to toxic epidermal necrolysis and shares many of the same triggers, notably drugs, but the inflammation is centred on and close to mucosal surfaces. Although mortality is low, acute morbidity is high and conjunctival involvement has the potential to cause blindness.

Index terms

  • Stevens-Johnson syndrome

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Foundation children elsewhere

  • EH63.0 – Drug-induced Stevens-Johnson syndrome

Sibling codes

  • EB13.1 – Toxic epidermal necrolysis
  • EB13.2 – Stevens-Johnson and toxic epidermal necrolysis overlap syndrome

Foundation entity

Stevens-Johnson syndrome – http://id.who.int/icd/entity/450167795

Part of: EB13: Stevens-Johnson syndrome or toxic epidermal necrolysis › 14: Diseases of the skin