ICD-11 MMS 2026-01
Pemphigus vulgaris Description Pemphigus vulgaris is a chronic autoimmune skin disease characterised by blister formation on the skin and the mucous membranes mediated by auto-antibodies to the desmosome components desmoglein 1 and 3.
Exclusions from above levels 1B72.0 – Bullous impetigo of the napkin area1F23.12 – Napkin candidosisEH71 – Dermatoses precipitated by drug therapyShow all Hide EH76 – Dermatoses associated with specific classes of medicationChild codes EB40.00 – Oral pemphigusEB40.0Y – Other specified pemphigus vulgarisEB40.0Z – Pemphigus vulgaris, unspecifiedSibling codes EB40.1 – Pemphigus foliaceusEB40.2 – Paraneoplastic pemphigusEB40.Y – Other specified pemphigusEB40.Z – Pemphigus, unspecifiedAllowed postcoordination axes Part of: EB40 : Pemphigus › 14 : Diseases of the skin
Source World Health Organization (WHO)
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under the Creative Commons Attribution-NoDerivatives 3.0 IGO licence (CC BY-ND 3.0 IGO).