EB40.0

ICD-11 MMS 2026-01

Pemphigus vulgaris

Description

Pemphigus vulgaris is a chronic autoimmune skin disease characterised by blister formation on the skin and the mucous membranes mediated by auto-antibodies to the desmosome components desmoglein 1 and 3.

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Child codes

  • EB40.00 – Oral pemphigus
  • EB40.0Y – Other specified pemphigus vulgaris
  • EB40.0Z – Pemphigus vulgaris, unspecified

Sibling codes

  • EB40.1 – Pemphigus foliaceus
  • EB40.2 – Paraneoplastic pemphigus
  • EB40.Y – Other specified pemphigus
  • EB40.Z – Pemphigus, unspecified

Foundation entity

Pemphigus vulgaris – http://id.who.int/icd/entity/278358681

Allowed postcoordination axes

Part of: EB40: Pemphigus › 14: Diseases of the skin