EB40.1

ICD-11 MMS 2026-01

Pemphigus foliaceus

Description

Pemphigus foliaceus is a chronic autoimmune skin disease characterised by superficial blister formation on the skin mediated by auto-antibodies to the desmosome component desmoglein 1.

Index terms

  • Pemphigus foliaceus
  • Superficial pemphigus
  • Pemphigus erythematosus
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  • Senear-Usher syndrome
  • Pemphigus herpetiformis
  • Endemic pemphigus foliaceus
  • Brazilian pemphigus
  • Fogo selvagem
  • Wild fire

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Sibling codes

  • EB40.0 – Pemphigus vulgaris
  • EB40.2 – Paraneoplastic pemphigus
  • EB40.Y – Other specified pemphigus
  • EB40.Z – Pemphigus, unspecified

Foundation entity

Pemphigus foliaceus – http://id.who.int/icd/entity/24246260

Part of: EB40: Pemphigus › 14: Diseases of the skin