EB42

ICD-11 MMS 2026-01

Linear IgA bullous dermatosis

Description

Linear IgA bullous dermatosis is an uncommon immunobullous disorder which occurs in both adults and children. It is characterised by linear deposition of IgA along the epidermal basement membrane. Although the clinical picture may resemble dermatitis herpetiformis, it is not associated with gluten enteropathy and it has different clinical and immunopathological attributes.

Index terms

  • Linear IgA bullous dermatosis
  • Linear IgA disease
  • Childhood linear IgA bullous dermatosis
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  • Chronic bullous disease of childhood
  • Linear IgA bullous dermatosis, childhood form
  • Adult linear IgA bullous dermatosis
  • Linear IgA bullous dermatosis, adult form

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Sibling codes

  • EB40 – Pemphigus
  • EB41 – Pemphigoid
  • EB43 – Epidermolysis bullosa acquisita
  • EB44 – Dermatitis herpetiformis
  • EB4Y – Other specified immunobullous disorder

Foundation entity

Linear IgA bullous dermatosis – http://id.who.int/icd/entity/1802341051

Part of: 14: Diseases of the skin