EB43

ICD-11 MMS 2026-01

Epidermolysis bullosa acquisita

Description

Epidermolysis bullosa acquisita is an acquired non-familial blistering disease characterised by the presence of autoantibodies to collagen VII at the epidermal basement membrane zone, as demonstrated by direct immunofluorescence. There is a wide spectrum of clinical manifestations including a trauma-induced variant and a more inflammatory variant.

Index terms

  • Epidermolysis bullosa acquisita
  • Acquired epidermolysis bullosa
  • EBA - [epidermolysis bullosa acquisita]
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  • Epidermolysis bullosa acquisita, Brunsting-Perry type

Excludes

  • http://id.who.int/icd/entity/1381715631 – Genetically-determined epidermolysis bullosa

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Sibling codes

  • EB40 – Pemphigus
  • EB41 – Pemphigoid
  • EB42 – Linear IgA bullous dermatosis
  • EB44 – Dermatitis herpetiformis
  • EB4Y – Other specified immunobullous disorder

Foundation entity

Epidermolysis bullosa acquisita – http://id.who.int/icd/entity/2034586329

Part of: 14: Diseases of the skin