EF40.10ICD-11 MMS 2026-01
Urticarial vasculitis
Description
An uncommon form of cutaneous leucocytoclastic vasculitis manifested by urticarial weals which, in contrast to those of chronic urticaria, are long-lasting and painful rather than itchy. A cause is often not identified. It may be associated with hypocomplementaemia and systemic inflammation (hypocomplementaemic urticarial vasculitis).
Index terms
- Urticarial vasculitis
- Normocomplementaemic urticarial vasculitis
Foundation children elsewhere
4A44.91– Hypocomplementaemic urticarial vasculitis
Sibling codes
EF40.1Y– Other specified vasculitis affecting small cutaneous blood vessels
Foundation entity
Urticarial vasculitis – http://id.who.int/icd/entity/975945467
Part of: EF40.1: Vasculitis affecting small cutaneous blood vessels › EF40: Vasculitis or capillaritis involving the skin › 14: Diseases of the skin