EF40.10

ICD-11 MMS 2026-01

Urticarial vasculitis

Description

An uncommon form of cutaneous leucocytoclastic vasculitis manifested by urticarial weals which, in contrast to those of chronic urticaria, are long-lasting and painful rather than itchy. A cause is often not identified. It may be associated with hypocomplementaemia and systemic inflammation (hypocomplementaemic urticarial vasculitis).

Index terms

  • Urticarial vasculitis
  • Normocomplementaemic urticarial vasculitis

Foundation children elsewhere

  • 4A44.91 – Hypocomplementaemic urticarial vasculitis

Sibling codes

  • EF40.1Y – Other specified vasculitis affecting small cutaneous blood vessels

Foundation entity

Urticarial vasculitis – http://id.who.int/icd/entity/975945467

Part of: EF40.1: Vasculitis affecting small cutaneous blood vessels › EF40: Vasculitis or capillaritis involving the skin › 14: Diseases of the skin