4A44.91ICD-11 MMS 2026-01
Hypocomplementaemic urticarial vasculitis
Description
Vasculitis accompanied by urticaria and hypocomplementemia affecting small vessels (i.e., capillaries, venules, or arterioles), and associated with anti-C1q antibodies. Glomerulonephritis, arthritis, obstructive pulmonary disease, and ocular inflammation are common.(Chapel Hill Consensus Conference, 2011)
Index terms
- Hypocomplementaemic urticarial vasculitis
- Anti-C1q vasculitis
Exclusions from above levels
Sibling codes
Foundation entity
Hypocomplementaemic urticarial vasculitis – http://id.who.int/icd/entity/629572966
Part of: 4A44.9: Immune complex small vessel vasculitis › 4A44: Vasculitis › 04: Diseases of the immune system