4A44.91

ICD-11 MMS 2026-01

Hypocomplementaemic urticarial vasculitis

Description

Vasculitis accompanied by urticaria and hypocomplementemia affecting small vessels (i.e., capillaries, venules, or arterioles), and associated with anti-C1q antibodies. Glomerulonephritis, arthritis, obstructive pulmonary disease, and ocular inflammation are common.(Chapel Hill Consensus Conference, 2011)

Index terms

  • Hypocomplementaemic urticarial vasculitis
  • Anti-C1q vasculitis

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A44.90 – Cryoglobulinaemic vasculitis
  • 4A44.92 – IgA vasculitis
  • 4A44.9Y – Other specified immune complex small vessel vasculitis
  • 4A44.9Z – Immune complex small vessel vasculitis, unspecified

Foundation entity

Hypocomplementaemic urticarial vasculitis – http://id.who.int/icd/entity/629572966

Part of: 4A44.9: Immune complex small vessel vasculitis › 4A44: Vasculitis › 04: Diseases of the immune system