FA23

ICD-11 MMS 2026-01

Adult-onset Still disease

Description

Adult onset Still's disease is a rare rheumatic condition characterised by a combination of symptoms, such as fever higher than 39 degrees C, cutaneous rash during fever peaks, joint or muscle pain, lymph node hypertrophy, increase of white blood cells (especially polymorphonuclear neutrophils) and abnormalities of liver metabolism.

Index terms

  • Adult-onset Still disease
  • Adult-onset Still disease, multiple sites
  • Adult-onset Still disease, shoulder region
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  • Adult-onset Still disease, acromioclavicular joint
  • Adult-onset Still disease, glenohumeral joint
  • Adult-onset Still disease, sternoclavicular joint
  • Adult-onset Still disease, upper arm
  • Adult-onset Still disease, elbow joint
  • Adult-onset Still disease, forearm
  • Adult-onset Still disease, wrist joint
  • Adult-onset Still disease, hand
  • Adult-onset Still disease, carpus
  • Adult-onset Still disease, fingers
  • Adult-onset Still disease, metacarpus
  • Adult-onset Still disease, pelvic region or thigh
  • Adult-onset Still disease, buttock
  • Adult-onset Still disease, hip joint
  • Adult-onset Still disease, lower leg
  • Adult-onset Still disease, knee joint
  • Adult-onset Still disease, ankle or foot
  • Adult-onset Still disease, metatarsus
  • Adult-onset Still disease, tarsus
  • Adult-onset Still disease, toes
  • Adult-onset Still disease, ankle joint
  • Adult-onset Still disease, other joints in foot
  • Adult-onset Still disease, head
  • Adult-onset Still disease, neck
  • Adult-onset Still disease, vertebral column
  • Erosive Adult-onset Still disease
  • Non-erosive Adult-onset Still disease

Excludes

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes
  • DA0E.8 – Temporomandibular joint disorders

Sibling codes

  • FA20 – Rheumatoid arthritis
  • FA21 – Psoriatic arthritis
  • FA22 – Polymyalgia rheumatica
  • FA24 – Juvenile idiopathic arthritis
  • FA25 – Gout
  • FA26 – Certain specified crystal arthropathies
  • FA27 – Certain specified inflammatory arthropathies
  • FA2Z – Inflammatory arthropathies, unspecified

Foundation entity

Adult-onset Still disease – http://id.who.int/icd/entity/549009522

Allowed postcoordination axes

Part of: 15: Diseases of the musculoskeletal system or connective tissue