FB80.0

ICD-11 MMS 2026-01

Fibrous dysplasia of bone

Description

Fibrous dysplasia of bone is a congenital non-hereditary benign bone disease, where normal bone is replaced by a fibrous-like tissue with immature osteogenesis. Bone lesions are mono- or polyostotic and may be associated with bone pain and fragility, leading to fractures. In some patients or bone sites, they are hypertrophic, and responsible for neurological complications.

Index terms

  • Fibrous dysplasia of bone
  • Mazabraud syndrome
  • McCune-Albright syndrome
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  • Albright-McCune-Sternberg syndrome
  • Fibrous dysplasia with pigmentary skin changes and precocious puberty
  • Monostotic fibrous dysplasia
  • Jaffe-Lichtenstein syndrome
  • fibrous dysplasia, site unspecified
  • localised osteitis fibrosa
  • monostotic dysplasia
  • osteitis fibrosa circumscripta
  • Monostotic fibrous dysplasia, multiple sites
  • Fibrous dysplasia (monostotic), multiple sites
  • Monostotic fibrous dysplasia, shoulder region
  • Fibrous dysplasia (monostotic), shoulder region
  • Monostotic fibrous dysplasia, clavicle
  • Fibrous dysplasia (monostotic), clavicle
  • Monostotic fibrous dysplasia, scapula
  • Fibrous dysplasia (monostotic), scapula
  • Monostotic fibrous dysplasia, acromioclavicular joint
  • Fibrous dysplasia (monostotic), acromioclavicular joint
  • Monostotic fibrous dysplasia, glenohumeral joint
  • Fibrous dysplasia (monostotic), glenohumeral joint
  • Monostotic fibrous dysplasia, sternoclavicular joint
  • Fibrous dysplasia (monostotic), sternoclavicular joint
  • Monostotic fibrous dysplasia, upper arm
  • Fibrous dysplasia (monostotic), upper arm
  • Monostotic fibrous dysplasia, humerus
  • Fibrous dysplasia (monostotic), humerus
  • Monostotic fibrous dysplasia, elbow joint
  • Fibrous dysplasia (monostotic), elbow joint
  • Monostotic fibrous dysplasia, forearm
  • Fibrous dysplasia (monostotic), forearm
  • Monostotic fibrous dysplasia, radius
  • Fibrous dysplasia (monostotic), radius
  • Monostotic fibrous dysplasia, ulna
  • Fibrous dysplasia (monostotic), ulna
  • Monostotic fibrous dysplasia, wrist joint
  • Fibrous dysplasia (monostotic), wrist joint
  • Monostotic fibrous dysplasia, hand
  • Fibrous dysplasia (monostotic), hand
  • Monostotic fibrous dysplasia, carpus
  • Fibrous dysplasia (monostotic), carpus
  • Monostotic fibrous dysplasia, fingers
  • Fibrous dysplasia (monostotic), fingers
  • Monostotic fibrous dysplasia, metacarpus
  • Fibrous dysplasia (monostotic), metacarpus
  • Monostotic fibrous dysplasia, pelvic region or thigh
  • Fibrous dysplasia (monostotic), pelvic region or thigh
  • Monostotic fibrous dysplasia, buttock
  • Fibrous dysplasia (monostotic), buttock
  • Monostotic fibrous dysplasia, femur
  • Fibrous dysplasia (monostotic), femur
  • Monostotic fibrous dysplasia, pelvis
  • Fibrous dysplasia (monostotic), pelvis
  • Monostotic fibrous dysplasia, hip joint
  • Fibrous dysplasia (monostotic), hip (joint)
  • Monostotic fibrous dysplasia, lower leg
  • Fibrous dysplasia (monostotic), lower leg
  • Monostotic fibrous dysplasia, fibula
  • Fibrous dysplasia (monostotic), fibula
  • Monostotic fibrous dysplasia, knee joint
  • Fibrous dysplasia (monostotic), knee joint
  • Monostotic fibrous dysplasia, tibia
  • Fibrous dysplasia (monostotic), tibia
  • Monostotic fibrous dysplasia, ankle or foot
  • Fibrous dysplasia (monostotic), ankle or foot
  • Monostotic fibrous dysplasia, metatarsus
  • Fibrous dysplasia (monostotic), metatarsus
  • Monostotic fibrous dysplasia, tarsus
  • Fibrous dysplasia (monostotic), tarsus
  • Monostotic fibrous dysplasia, toes
  • Fibrous dysplasia (monostotic), toes
  • Monostotic fibrous dysplasia, ankle joint
  • Fibrous dysplasia (monostotic), ankle joint
  • Monostotic fibrous dysplasia, other joints in foot
  • Fibrous dysplasia (monostotic), other joints in foot
  • Monostotic fibrous dysplasia, head
  • Fibrous dysplasia (monostotic), head
  • Monostotic fibrous dysplasia, neck
  • Fibrous dysplasia (monostotic), neck
  • Monostotic fibrous dysplasia, ribs
  • Fibrous dysplasia (monostotic), ribs
  • Monostotic fibrous dysplasia, skull
  • Fibrous dysplasia (monostotic), skull
  • Monostotic fibrous dysplasia, trunk
  • Fibrous dysplasia (monostotic), trunk
  • Monostotic fibrous dysplasia, vertebral column
  • Fibrous dysplasia (monostotic), vertebral column
  • Polyostotic fibrous dysplasia
  • PFD - [polyostotic fibrous dysplasia]
  • osteitis fibrosa disseminata
  • polyostotic fibrodysplasia
  • polyostotic fibrous dysplasia of bone
  • Fibrous dysplasia of jaw
  • Familial fibrous dysplasia of jaw

Exclusions from above levels

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  • LD24.10 – Osteopetrosis
  • LD24.11 – Osteopoikilosis
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes
  • DA0E.8 – Temporomandibular joint disorders

Sibling codes

  • FB80.1 – Skeletal fluorosis
  • FB80.2 – Osteitis condensans
  • FB80.3 – Hyperostosis of skull
  • FB80.4 – Osteosclerosis
  • FB80.5 – Solitary bone cyst
  • FB80.6 – Aneurysmal bone cyst
  • FB80.7 – Malunion of fracture
  • FB80.8 – Nonunion of fracture
  • FB80.9 – Delayed union of fracture
  • FB80.A – Stress fracture, not elsewhere classified
  • FB80.B – Pathological fracture
  • FB80.Y – Other specified disorders of bone density or structure
  • FB80.Z – Disorder of bone density or structure, unspecified

Foundation entity

Fibrous dysplasia of bone – http://id.who.int/icd/entity/1704766818

Allowed postcoordination axes

Part of: FB80: Certain specified disorders of bone density or structure › 15: Diseases of the musculoskeletal system or connective tissue