FB80.0ICD-11 MMS 2026-01
Fibrous dysplasia of bone
Description
Fibrous dysplasia of bone is a congenital non-hereditary benign bone disease, where normal bone is replaced by a fibrous-like tissue with immature osteogenesis. Bone lesions are mono- or polyostotic and may be associated with bone pain and fragility, leading to fractures. In some patients or bone sites, they are hypertrophic, and responsible for neurological complications.
Index terms
- Fibrous dysplasia of bone
- Mazabraud syndrome
- McCune-Albright syndrome
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- Albright-McCune-Sternberg syndrome
- Fibrous dysplasia with pigmentary skin changes and precocious puberty
- Monostotic fibrous dysplasia
- Jaffe-Lichtenstein syndrome
- fibrous dysplasia, site unspecified
- localised osteitis fibrosa
- monostotic dysplasia
- osteitis fibrosa circumscripta
- Monostotic fibrous dysplasia, multiple sites
- Fibrous dysplasia (monostotic), multiple sites
- Monostotic fibrous dysplasia, shoulder region
- Fibrous dysplasia (monostotic), shoulder region
- Monostotic fibrous dysplasia, clavicle
- Fibrous dysplasia (monostotic), clavicle
- Monostotic fibrous dysplasia, scapula
- Fibrous dysplasia (monostotic), scapula
- Monostotic fibrous dysplasia, acromioclavicular joint
- Fibrous dysplasia (monostotic), acromioclavicular joint
- Monostotic fibrous dysplasia, glenohumeral joint
- Fibrous dysplasia (monostotic), glenohumeral joint
- Monostotic fibrous dysplasia, sternoclavicular joint
- Fibrous dysplasia (monostotic), sternoclavicular joint
- Monostotic fibrous dysplasia, upper arm
- Fibrous dysplasia (monostotic), upper arm
- Monostotic fibrous dysplasia, humerus
- Fibrous dysplasia (monostotic), humerus
- Monostotic fibrous dysplasia, elbow joint
- Fibrous dysplasia (monostotic), elbow joint
- Monostotic fibrous dysplasia, forearm
- Fibrous dysplasia (monostotic), forearm
- Monostotic fibrous dysplasia, radius
- Fibrous dysplasia (monostotic), radius
- Monostotic fibrous dysplasia, ulna
- Fibrous dysplasia (monostotic), ulna
- Monostotic fibrous dysplasia, wrist joint
- Fibrous dysplasia (monostotic), wrist joint
- Monostotic fibrous dysplasia, hand
- Fibrous dysplasia (monostotic), hand
- Monostotic fibrous dysplasia, carpus
- Fibrous dysplasia (monostotic), carpus
- Monostotic fibrous dysplasia, fingers
- Fibrous dysplasia (monostotic), fingers
- Monostotic fibrous dysplasia, metacarpus
- Fibrous dysplasia (monostotic), metacarpus
- Monostotic fibrous dysplasia, pelvic region or thigh
- Fibrous dysplasia (monostotic), pelvic region or thigh
- Monostotic fibrous dysplasia, buttock
- Fibrous dysplasia (monostotic), buttock
- Monostotic fibrous dysplasia, femur
- Fibrous dysplasia (monostotic), femur
- Monostotic fibrous dysplasia, pelvis
- Fibrous dysplasia (monostotic), pelvis
- Monostotic fibrous dysplasia, hip joint
- Fibrous dysplasia (monostotic), hip (joint)
- Monostotic fibrous dysplasia, lower leg
- Fibrous dysplasia (monostotic), lower leg
- Monostotic fibrous dysplasia, fibula
- Fibrous dysplasia (monostotic), fibula
- Monostotic fibrous dysplasia, knee joint
- Fibrous dysplasia (monostotic), knee joint
- Monostotic fibrous dysplasia, tibia
- Fibrous dysplasia (monostotic), tibia
- Monostotic fibrous dysplasia, ankle or foot
- Fibrous dysplasia (monostotic), ankle or foot
- Monostotic fibrous dysplasia, metatarsus
- Fibrous dysplasia (monostotic), metatarsus
- Monostotic fibrous dysplasia, tarsus
- Fibrous dysplasia (monostotic), tarsus
- Monostotic fibrous dysplasia, toes
- Fibrous dysplasia (monostotic), toes
- Monostotic fibrous dysplasia, ankle joint
- Fibrous dysplasia (monostotic), ankle joint
- Monostotic fibrous dysplasia, other joints in foot
- Fibrous dysplasia (monostotic), other joints in foot
- Monostotic fibrous dysplasia, head
- Fibrous dysplasia (monostotic), head
- Monostotic fibrous dysplasia, neck
- Fibrous dysplasia (monostotic), neck
- Monostotic fibrous dysplasia, ribs
- Fibrous dysplasia (monostotic), ribs
- Monostotic fibrous dysplasia, skull
- Fibrous dysplasia (monostotic), skull
- Monostotic fibrous dysplasia, trunk
- Fibrous dysplasia (monostotic), trunk
- Monostotic fibrous dysplasia, vertebral column
- Fibrous dysplasia (monostotic), vertebral column
- Polyostotic fibrous dysplasia
- PFD - [polyostotic fibrous dysplasia]
- osteitis fibrosa disseminata
- polyostotic fibrodysplasia
- polyostotic fibrous dysplasia of bone
- Fibrous dysplasia of jaw
- Familial fibrous dysplasia of jaw
Exclusions from above levels
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LD24.10– OsteopetrosisLD24.11– Osteopoikilosis01– Certain infectious or parasitic diseases05– Endocrine, nutritional or metabolic diseases18– Complications of pregnancy, childbirth and the puerperium19– Certain conditions originating in the perinatal period22– Injury, poisoning or certain other consequences of external causesDA0E.8– Temporomandibular joint disorders
Sibling codes
FB80.1– Skeletal fluorosisFB80.2– Osteitis condensansFB80.3– Hyperostosis of skullFB80.4– OsteosclerosisFB80.5– Solitary bone cystFB80.6– Aneurysmal bone cystFB80.7– Malunion of fractureFB80.8– Nonunion of fractureFB80.9– Delayed union of fractureFB80.A– Stress fracture, not elsewhere classifiedFB80.B– Pathological fractureFB80.Y– Other specified disorders of bone density or structureFB80.Z– Disorder of bone density or structure, unspecified
Foundation entity
Fibrous dysplasia of bone – http://id.who.int/icd/entity/1704766818
Allowed postcoordination axes
Part of: FB80: Certain specified disorders of bone density or structure › 15: Diseases of the musculoskeletal system or connective tissue