GB41

ICD-11 MMS 2026-01

Nephrotic syndrome

Description

A condition characterised by severe proteinuria, greater than 3.5 g/day in an average adult. The substantial loss of protein in the urine results in hypoalbuminaemia and generalised oedema. There is also usually hyperlipidaemia. Other manifestations of glomerular disease may be present. There are many possible causes and renal histological appearances. Possible complications include vascular thrombosis, infections, malnutrition and renal failure.

Index terms

  • Nephrotic syndrome
  • NS - [nephrotic syndrome]
  • glomerular lesion nephrosis
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  • nephrosis NOS
  • nephrosis syndrome
  • Steroid sensitive nephrotic syndrome
  • Idiopathic steroid-sensitive nephrotic syndrome
  • Steroid resistant nephrotic syndrome
  • Galloway Mowat syndrome
  • Pierson syndrome
  • Multi-drug resistant nephrotic syndrome
  • Minimal change glomerulonephritis
  • MCGN - [minimal change glomerulonephritis]
  • foot process disease
  • Congenital Finnish nephrosis
  • CNF - [Finnish congenital nephrotic syndrome]
  • Finnish congenital nephrotic syndrome
  • Epstein's nephrosis
  • Congenital nephrotic syndrome
  • acute congenital nephrosis
  • congenital nephrosis
  • Familial nephrotic syndrome
  • Lipid nephrosis
  • lipoid nephrosis
  • Nephritis with oedema
  • glomerulonephritis with oedema NOS
  • nephritis with oedema NOS
  • Acute nephrosis syndrome
  • acute nephrosis
  • Familial idiopathic steroid-resistant nephrotic syndrome
  • Congenital membranous nephropathy due to fetomaternal anti-neutral endopeptidase alloimmunization

Exclusions from above levels

  • BA02 – Hypertensive renal disease
  • JA20.2 – Glomerular diseases with pre-existing hypertension in the puerperium
  • JB44.Y – Glomerular diseases in puerperium
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  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • GB40 – Nephritic syndrome
  • GB42 – Persistent proteinuria or albuminuria
  • GB4Y – Other specified glomerular diseases
  • GB4Z – Glomerular diseases, unspecified

Foundation entity

Nephrotic syndrome – http://id.who.int/icd/entity/1184209951

Allowed postcoordination axes

Part of: 16: Diseases of the genitourinary system