KA07.0

ICD-11 MMS 2026-01

Neonatal lupus erythematosus

Description

Neonatal lupus erythematosus results from trans-placental transfer of maternal antibodies, in particular anti-Ro/SSA and anti La/SSB. It manifests with an erythematous rash which may be obviously photosensitive and is closely associated with congenital heart block. The mother may have known lupus, especially subacute cutaneous lupus erythematosus, but she may be asymptomatic. The rash normally subsides within the first few months of life.

Coding note from above levels

These codes are for use when the listed maternal conditions are specified as the cause of confirmed morbidity or potential morbidity which have their origin in the perinatal period (before birth through the first 28 days after birth). Use additional code to identify the condition in the fetus or newborn.

Conditions arising in the perinatal period, even though death or morbidity occurs later, should, as far as possible, be coded to chapter 19, which takes precedence over chapters containing codes for diseases by their anatomical site. For children less than 28 days old, assume that a reported condition developed in the perinatal period, unless the duration is stated and the onset was after the first completed week of life.

Index terms

  • Neonatal lupus erythematosus

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases - acquired after birth
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 08 – Certain congenital diseases of the nervous system
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • 3A10 – Hereditary haemolytic anaemia
  • 4A01.03 – Transient hypogammaglobulinaemia of infancy
  • 9B71.3 – Retinopathy of prematurity
  • BC43 – congenital cardiomyopathy
  • DA93.0 – Paralytic ileus
  • EA50.Z – Pemphigus neonatorum
  • EH40.00 – Cradle cap
  • http://id.who.int/icd/entity/588616678 – Gastroenteritis or colitis of infectious origin
  • http://id.who.int/icd/entity/609214049 – Congenital gonococcal infection

Sibling codes

  • KA07.1 – Neonatal pemphigus
  • KA07.Y – Other specified neonatal dermatoses due to maternal antibodies

Foundation entity

Neonatal lupus erythematosus – http://id.who.int/icd/entity/213855225

Part of: KA07: Neonatal dermatoses due to maternal antibodies › 19: Certain conditions originating in the perinatal period