KA64.0

ICD-11 MMS 2026-01

Congenital toxoplasmosis

Description

A disease caused by an infection with the protozoan parasite Toxoplasma gondii in utero. This disease is characterised by chorioretinitis, hydrocephalus, intracranial calcifications, anaemia, or neurological deficits that develop after birth. This disease may present at birth with jaundice, premature birth, hepatosplenomegaly, myocarditis, pneumonitis, or rash. Transmission is by vertical transmission. In the fetus, confirmation is by identification of Toxoplasma gondii in amniotic fluid; in the neonate, confirmation is by identification of Toxoplasma gondii in body fluids or tissues, or detection of antibodies against Toxoplasma gondii.

Coding note from above levels

Conditions arising in the perinatal period, even though death or morbidity occurs later, should, as far as possible, be coded to chapter 19, which takes precedence over chapters containing codes for diseases by their anatomical site. For children less than 28 days old, assume that a reported condition developed in the perinatal period, unless the duration is stated and the onset was after the first completed week of life.

Index terms

  • Congenital toxoplasmosis
  • Congenital toxoplasma encephalitis
  • congenital encephalitis due to Toxoplasma gondii
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  • congenital encephalitis in toxoplasmosis
  • Hydrocephalus due to congenital toxoplasmosis

Exclusions from above levels

  • 1A60 – Congenital syphilis
  • 1C15 – Tetanus neonatorum
  • KB88 – Necrotising enterocolitis of newborn
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  • 1C62.0 – Asymptomatic human immunodeficiency virus infection
  • http://id.who.int/icd/entity/1000704511 – human immunodeficiency virus [HIV] disease
  • http://id.who.int/icd/entity/588616678 – Gastroenteritis or colitis of infectious origin
  • http://id.who.int/icd/entity/609214049 – congenital gonococcal infection
  • MA14.0 – Laboratory evidence of human immunodeficiency virus
  • 01 – Certain infectious or parasitic diseases - acquired after birth
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
  • 08 – Certain congenital diseases of the nervous system
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • 3A10 – Hereditary haemolytic anaemia
  • 4A01.03 – Transient hypogammaglobulinaemia of infancy
  • 9B71.3 – Retinopathy of prematurity
  • BC43 – congenital cardiomyopathy
  • DA93.0 – Paralytic ileus
  • EA50.Z – Pemphigus neonatorum
  • EH40.00 – Cradle cap

Sibling codes

  • KA64.2 – Congenital malaria
  • KA64.Y – Other specified parasitic diseases in the fetus or newborn
  • KA64.Z – Parasitic diseases in the fetus or newborn, unspecified

Foundation entity

Congenital toxoplasmosis – http://id.who.int/icd/entity/1194018225

Allowed postcoordination axes

Part of: KA64: Parasitic diseases in the fetus or newborn › 19: Certain conditions originating in the perinatal period