KA88

ICD-11 MMS 2026-01

Disseminated intravascular coagulation of fetus or newborn

Description

Neonatal purpura fulminans is a potentially lethal disorder characterised by progressive haemorrhagic necrosis of the skin associated with cutaneous vascular thrombosis. It is usually due to a genetically transmitted thrombophilic disorder: most commonly homozygous deficiency of protein C or, less frequently, protein S.

Coding note from above levels

Conditions arising in the perinatal period, even though death or morbidity occurs later, should, as far as possible, be coded to chapter 19, which takes precedence over chapters containing codes for diseases by their anatomical site. For children less than 28 days old, assume that a reported condition developed in the perinatal period, unless the duration is stated and the onset was after the first completed week of life.

Index terms

  • Disseminated intravascular coagulation of fetus or newborn
  • Neonatal purpura fulminans

Exclusions from above levels

  • 3A10 – Hereditary haemolytic anaemia
  • 5C58.00 – Crigler-Najjar syndrome
  • 5C58.01 – Gilbert syndrome
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  • 5C58.02 – Dubin-Johnson syndrome
  • LB20.22 – Congenital stenosis or stricture of bile ducts
  • 01 – Certain infectious or parasitic diseases - acquired after birth
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
  • 08 – Certain congenital diseases of the nervous system
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • 4A01.03 – Transient hypogammaglobulinaemia of infancy
  • 9B71.3 – Retinopathy of prematurity
  • BC43 – congenital cardiomyopathy
  • DA93.0 – Paralytic ileus
  • EA50.Z – Pemphigus neonatorum
  • EH40.00 – Cradle cap
  • http://id.who.int/icd/entity/588616678 – Gastroenteritis or colitis of infectious origin
  • http://id.who.int/icd/entity/609214049 – Congenital gonococcal infection

Sibling codes

  • KA80 – Fetal blood loss
  • KA81 – Umbilical haemorrhage of newborn
  • KA82 – Intracranial nontraumatic haemorrhage of fetus or newborn
  • KA83 – Certain specified neonatal haemorrhages
  • KA84 – Haemolytic disease of fetus or newborn
  • KA85 – Hydrops fetalis due to haemolytic disease
  • KA86 – Neonatal kernicterus
  • KA87 – Neonatal hyperbilirubinaemia
  • KA89 – Transient neonatal thrombocytopaenia
  • KA8A – Polycythaemia neonatorum
  • KA8B – Anaemia of prematurity
  • KA8C – Congenital hypoplastic anaemia
  • KA8D – Transient neonatal neutropaenia
  • KA8E – Alloimmune neonatal neutropaenia
  • KA8F – Neonatal vitamin K deficiency
  • KA8Y – Other specified haemorrhagic or haematological disorders of fetus or newborn
  • KA8Z – Haemorrhagic or haematological disorders of fetus or newborn, unspecified

Foundation entity

Disseminated intravascular coagulation of fetus or newborn – http://id.who.int/icd/entity/742410330

Part of: 19: Certain conditions originating in the perinatal period