KB27.0

ICD-11 MMS 2026-01

Interstitial emphysema originating in the perinatal period

Description

Escape of air into the interstitium, lymphatics and venous circulation of the lungs resulting from rupture of small airways associated with a characteristic cystic appearance on chest X-ray, almost exclusively seen in preterm infants receiving mechanical ventilation

Coding note from above levels

Conditions arising in the perinatal period, even though death or morbidity occurs later, should, as far as possible, be coded to chapter 19, which takes precedence over chapters containing codes for diseases by their anatomical site. For children less than 28 days old, assume that a reported condition developed in the perinatal period, unless the duration is stated and the onset was after the first completed week of life.

Index terms

  • Interstitial emphysema originating in the perinatal period
  • CLE - [congenital lobar emphysema]
  • congenital atrophic emphysema
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  • congenital emphysema
  • congenital interlobular emphysema
  • congenital interstitial emphysema
  • congenital interstitial pulmonary emphysema
  • congenital lung emphysema
  • congenital obstructive emphysema
  • congenital obstructive pulmonary emphysema
  • congenital pulmonary emphysema
  • congenital senile emphysema
  • emphysema of fetus or newborn
  • infantile lobar emphysema
  • interstitial emphysema, perinatal period
  • Chronic congenital interstitial emphysema
  • chronic congenital emphysema
  • chronic congenital obstructive pulmonary emphysema

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases - acquired after birth
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 08 – Certain congenital diseases of the nervous system
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • 3A10 – Hereditary haemolytic anaemia
  • 4A01.03 – Transient hypogammaglobulinaemia of infancy
  • 9B71.3 – Retinopathy of prematurity
  • BC43 – congenital cardiomyopathy
  • DA93.0 – Paralytic ileus
  • EA50.Z – Pemphigus neonatorum
  • EH40.00 – Cradle cap
  • http://id.who.int/icd/entity/588616678 – Gastroenteritis or colitis of infectious origin
  • http://id.who.int/icd/entity/609214049 – Congenital gonococcal infection

Sibling codes

  • KB27.1 – Pneumothorax originating in the perinatal period
  • KB27.2 – Pneumomediastinum originating in the perinatal period
  • KB27.3 – Pneumopericardium originating in the perinatal period
  • KB27.4 – Pneumoperitoneum, originating in the perinatal period, due to primary pulmonary air leak syndromes
  • KB27.Y – Other specified pulmonary air leak or related conditions originating in the perinatal period
  • KB27.Z – Pulmonary air leak or related conditions originating in the perinatal period, unspecified

Foundation entity

Interstitial emphysema originating in the perinatal period – http://id.who.int/icd/entity/788906923

Part of: KB27: Pulmonary air leak or related conditions originating in the perinatal period › 19: Certain conditions originating in the perinatal period