KC01

ICD-11 MMS 2026-01

Congenital renal failure

Description

A severe irreversible decline in the ability of kidneys to remove wastes, concentrate urine, and maintain electrolyte balance; blood pressure; and calcium metabolism which existed at, or often before, birth.

Coding note from above levels

Conditions arising in the perinatal period, even though death or morbidity occurs later, should, as far as possible, be coded to chapter 19, which takes precedence over chapters containing codes for diseases by their anatomical site. For children less than 28 days old, assume that a reported condition developed in the perinatal period, unless the duration is stated and the onset was after the first completed week of life.

Index terms

  • Congenital renal failure
  • Uraemia of newborn
  • congenital kidney insufficiency
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  • congenital renal insufficiency
  • congenital uaremia
  • newborn anuria
  • newborn uraemia
  • newborn uraemic coma

Inclusions

  • Uraemia of newborn

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases - acquired after birth
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 08 – Certain congenital diseases of the nervous system
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • 3A10 – Hereditary haemolytic anaemia
  • 4A01.03 – Transient hypogammaglobulinaemia of infancy
  • 9B71.3 – Retinopathy of prematurity
  • BC43 – congenital cardiomyopathy
  • DA93.0 – Paralytic ileus
  • EA50.Z – Pemphigus neonatorum
  • EH40.00 – Cradle cap
  • http://id.who.int/icd/entity/588616678 – Gastroenteritis or colitis of infectious origin
  • http://id.who.int/icd/entity/609214049 – Congenital gonococcal infection

Sibling codes

  • KC00 – Congenital hydrocele
  • KC0Y – Other specified genitourinary system disorders specific to the perinatal or neonatal period
  • KC0Z – Genitourinary system disorders specific to the perinatal or neonatal period, unspecified

Foundation entity

Congenital renal failure – http://id.who.int/icd/entity/1635967154

Allowed postcoordination axes

Part of: 19: Certain conditions originating in the perinatal period